NURSING CARE PROCESS IN A PATIENT WITH HEMOPHILIA TYPE A - CLINICAL CASE REPORT
DOI:
https://doi.org/10.70187/recisatec.v4i2.371Keywords:
Hemophilia A. Factor VIII. Risk factors. Complications. Prevalence. Nursing care.Abstract
Hemophilia A is a genetic or orphan disease of low prevalence, since its occurrence is considered singular and lacks therapeutic options, depending on the severity of hemophilia should be subjected to different treatments, either prophylaxis or on demand. These have affected the population for decades, being one of the most important hemorrhagic diseases and with the highest morbidity and mortality worldwide, it is an alteration in the coagulation cascade, directly affecting factor VIII, preventing hemostasis in the face of possible bleeding; these can occur in different body areas, the most vulnerable being the joints and muscles. We present the case of a 10-year-old male patient diagnosed with severe hemophilia A who was treated with Octanate, a complex coagulant anti-inhibitor, activated Eptacog alfa and Emicizumab, with the role of nursing being a fundamental axis to achieve the objective of improving the patient's quality of life.
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